Tracheobronchomegaly (Mounier-Kuhn Syndrome)
نویسندگان
چکیده
Tracheobronchomegaly (Mounier-Kuhn syndrome) is defined as marked cystic tracheobronchial dilatation. Tracheobronchomegaly (TBM) is a rare condition primarily effecting men between the ages of 40 to 50 years. The etiology of TBM is unknown. Pathologically, there is atrophy of the muscular and elastic elements of the trachea and central bronchi. The diagnosis of TBM and the associated pathology of the respiratory system are primarily based on radiographic examinations such as plain chest radiographs and CT scans. We report two cases of TBM with a history of recurrent lower respiratory tract infections.
منابع مشابه
Case Report: Mounier–Kuhn Syndrome
Tracheobronchomegaly (TBM) or Mounier Kuhn syndrome is a rare disorder of uncertain aetiology characterized by marked dilatation of trachea and bronchi and recurrent lower respiratory tract infection. We report a case in a 20 year old male presenting with recurrent lower respiratory tract infection.
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